Assessing and managing people with sickle cell disease presenting with vaso-occlusive crisis in the emergency department
CPD    

Assessing and managing people with sickle cell disease presenting with vaso-occlusive crisis in the emergency department

Diana De Senior lecturer in adult nursing, College of Biomedical and Life Sciences, Cardiff University, Wales
Indu Thakur Consultant paediatric haematologist, lead for red blood cell disorders, Noah’s Ark Children’s Hospital, Cardiff, Wales

Why you should read this article:
  • To increase your knowledge and understanding of sickle cell disease and its acute manifestations

  • To understand how to assess and manage patients with vaso-occlusive crisis in the emergency department

  • To contribute towards revalidation as part of your 35 hours of CPD (UK readers)

  • To contribute towards your professional development and local registration renewal requirements (non-UK readers)

Sickle cell disease is a group of inherited blood disorders characterised by atypical haemoglobin molecule structures (haemoglobin S) which can manifest as painful vaso-occlusive crises, chronic anaemia and progressive organ damage. This article aims to raise greater awareness of sickle cell disease, its acute manifestations and the potential for rapid clinical deterioration that can occur in patients with this condition. The article outlines the main aspects of the assessment and management of patients presenting to the emergency department (ED) with vaso-occlusive crisis, describes the barriers to effective care that they commonly experience and explains how their care could be improved. The authors emphasise the importance of timely management of these patients by ED staff, including emergency nurses.

Emergency Nurse. doi: 10.7748/en.2022.e2117

Peer review

This article has been subject to external double-blind peer review and checked for plagiarism using automated software

@TheDianaDe

Correspondence

DeD@cardiff.ac.uk

Conflict of interest

None declared

De D, Thakur I (2022) Assessing and managing people with sickle cell disease presenting with vaso-occlusive crisis in the emergency department. Emergency Nurse. doi: 10.7748/en.2022.e2117

Published online: 12 January 2022

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